肺粘液性嚢胞腺癌：異常な症例と文献レビュー

Pulmonary mucinous cystadenocarcinoma: an unusual presentation and literature review.

• Pandi Todhe
• Nishant Sharma
• Ajay Shetty
• Pius Ochieng

抄録

嚢胞性肺疾患は、遺伝性／先天性疾患、全身性疾患、感染性疾患などの中でも特に遺伝性／先天性疾患に起因する異質な肺疾患群である。肺粘液性嚢胞性新生物はムチンを豊富に含む新生物性嚢胞性疾患のスペクトラムであり，その中でも肺粘液性嚢胞腺癌（PMC）はまれな悪性サブタイプである．呼吸困難，咳嗽，倦怠感，体重減少を呈した66歳男性の1例を紹介する．胸部画像診断で多数の空洞病変を認め，肺生検でPMCと診断された．緩和化学療法を受け，1年後に死亡した．我々は、我々の症例を含む26例の報告に基づいて、PMCの文献レビューを行う。

Cystic lung disease is a group of heterogeneous pulmonary diseases resulting from hereditary/congenital disorders, systemic disorders and infectious causes among others. Pulmonary mucinous cystic neoplasia is a spectrum of neoplastic cystic diseases with abundant mucin, of which pulmonary mucinous cystadenocarcinoma (PMC) is a rare malignant subtype. We present a case of a 66-year-old man who presented with dyspnoea, cough, fatigue and weight loss. Imaging of his chest showed numerous cavitary lesions, and the diagnosis of PMC was made based on lung biopsy. He received palliative chemotherapy and died 1 year later. We present a literature review of PMC based on 26 reported cases, including our own.

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